The aim of this study was to report a case of unilateral fibrous dysplasia in the maxilla, in the palate region, by using computed tomography. A vestibular approach was used to remove the tissue and histopathological picture of the 4 patients showed loosely arranged curvilinear trabeculae with fibrous elements leading to a diagnosis of fibrous dysplasia. Isolated fibrous dysplasia of the inferior turbinate. Fd occurs in monostotic or polyostotic forms, and the latter may be associated with mccunealbright syndrome, which is the most severe form of polyostotic fd. Summary osteofibrous displasia is an infrequent benign tumor in head and neck. Fibrous dysplasia fd is a rare fibroosseous lesion characterized by progressive replacement of normal bone elements with benign cellular fibrous connective tissue. Abstract headache is one of the most frequent symptoms in medicine that can be classified as primary, like tensional headache and migraine or secondary as in tumors, infections, or other causes. May 24, 2012 the management of sinus and nasal congestion includes nasal saline spray, nasal steroid spray, antihistamines for those with seasonal allergies, and antibiotics for suspected bacterial sinus infections. Cefalea, cornete medio, displasia fibrosa, cefalea rinogenica. Usually asymptomatic, its treatment is surgical when it creates an important facial. Displasia fibrosa diagnostico y tratamiento mayo clinic. The fibrous dysplasia is a benign bone disease, of slow growth and unknown etiology. Seram 2014 s12 anatomia y patologia tumoral benigna. Fibrous dysplasia fd is a benign skeletal disorder in which abnormally overgrowing bony lesion replaces normal bone.
Nasal disorders fibrous dysplasia middle turbinate. Displasia fibrosa craneofacial avanzada por remodelacion. The patient was forwarded to the surgical center for the lesion biopsy. A displasia fibrosa e uma lesao ossea com etiologia ainda desconhecida. Fibrous dysplasia fd is a nonneoplastic tumorlike congenital process, manifested as a localized defect in osteoblastic differentiation and maturation, with the replacement of normal bone with large fibrous stroma and islands of immature woven bone. Displasia fibrosa genetic and rare diseases information. Abstract fibrous dysplasia of bone fibrous dysplasia of bone is a noninherited developmental anomaly of bone characterized by abnormal proliferation of fibroblasts and differentiation of osteoblasts that cause a replacement of trabeculous bone by fibrous connective tissue. The access was intraoral through caldwellluc surgery and the lesion fragment was removed for histopathological study, which revealed a compatible picture with fibrous dysplasia. A displasia fibrosa e classificado como doencas tumorais pode ser local ou generalizada, atingindo um ou mais ossos. Fibrous dysplasia is a disorder where normal bone and marrow is replaced with fibrous tissue, resulting in formation of bone that is weak and prone to expansion.
Rbcp surgical approach to the treatment of craniofacial. Consultation with an otolaryngologist may be necessary for persistent congestion and chronic sinus infections. The craniofacial bones are involved in about 10% of subjects. The skull is a frequent site of the pathologic process now known as fibrous dysplasia and the skull changes are often the only manifestation of the disease. The involvement of the craniofacial skeleton is not uncommon and, generally, produces facial asymmetries. O envolvimento do esqueleto craniofacial nao e incomum e, geralmente, produz assimetrias faciais. It is mainly located in the maxillary bone, while its nasal. Pdf craniofacial fibrous dysplasia addressed through the. Tomografia computadorizada dos seios da face no plano axial. In this article we report the case of a patient with fibrous dysplasia occupying the entire left maxillary sinus. A displasia fibrosa e uma alteracao fibroossea benig. Fibrous dysplasia is an idiopathic benign disorder that is most frequent in young adults.
The skull and facial bones are affected in 10%25% of the patients with monostotic fibrous dysplasia, but it is uncommon in the nasal fossa. Fibrous dysplasia has a varied radiographic appearance. Findings in a 25 yearold male consistent with fibrous dysplasia. We report a 27 year old male patient, with a history of nasal septum. As a result, most complications result from fracture, deformity, functional impairment, and pain. Fd can affect one bone monostotic form or multiple bones polyostotic form. Craniofacial fibrous dysplasia addressed through the intraoral and nasal access. Fibrous dysplasia of the skull and its differential. It is located mainly in the maxillary bone, affecting with certain frequency the perinasal cavities. Displasia fibrosa causas, sintomas, diagnostico e tratamento. Fibrous dysplasia of middle turbinate associated with widal syndrome. Caracteristicas tomograficas da displasia fibrosa craniofacial. This lesion seems to originate from the nasal turbinates and paranasal sinus walls at the right side. Displasia fibrosa osea poliostotica generalizada con.
443 968 819 1289 222 1510 1302 1554 812 332 848 634 615 172 332 1078 1613 1141 153 1544 875 1609 386 1639 941 1378 260 794 1316 918 1305 162 866 355 815 820 751 1100